Case Reports
Vol. 18 No. 1 (2026)
Unusual presentation of skin nodule in a child: a case report of primary cutaneous CD4+ small/medium T-cell lymphoproliferative disorder and literature review
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All claims expressed in this article are solely those of the authors and do not necessarily represent those of their affiliated organizations, or those of the publisher, the editors and the reviewers. Any product that may be evaluated in this article or claim that may be made by its manufacturer is not guaranteed or endorsed by the publisher.
Received: 8 October 2024
Accepted: 3 May 2025
Accepted: 3 May 2025
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Primary cutaneous CD4+ small/medium T-cell lymphoproliferative disorder (SMPLPD) is a rare, definite type of cutaneous T-cell lymphoma (CTCL) that accounts for 6% of all primary CTCLs. Characteristically, this lymphoproliferative disorder presents as a solitary nodule, plaque, or tumor, generally on the face, neck, or upper trunk. We report a case of SMPLPD presenting as a facial nodule in a 6-year-old Saudi girl. The patient was successfully treated with complete excision and showed full resolution, with no recurrence at 6-month follow-up.
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Citations
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Aloraifi L, Alotaibi H, Bajawi S, Bajawi N, Almulhim A, Shaikh L. Unusual presentation of skin nodule in a child: a case report of primary cutaneous CD4+ small/medium T-cell lymphoproliferative disorder and literature review. Dermatol Reports [Internet]. 2025 May 9 [cited 2026 May 21];18(1). Available from: https://journals.pagepress.net/dr/article/view/10163
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